Keck School Faculty

Reduced Forced Vital Capacity and the Number of Chest Wall Surgeries are Associated with Decreased Exercise Capacity in Children with Congenital Heart Disease Pediatr Cardiol. 2022 Jan; 43(1):54-61. . View in PubMed

Am J Hematol. 2021 01; 96(1):31-39. . View in PubMed

Vasoconstriction Response to Mental Stress in Sickle Cell Disease: The Role of the Cardiac and Vascular Baroreflexes Front Physiol. 2021; 12:698209. . View in PubMed

Loss of alpha-globin genes in human subjects is associated with improved nitric oxide-mediated vascular perfusion Am J Hematol. 2021 03 01; 96(3):277-281. . View in PubMed

Pediatr Pulmonol. 2020 Oct 02. . View in PubMed

Comparison of SIMV+PS and AC modes in chronically ventilated children and effects on speechg Pediatr Pulmonol. 2020 Oct 02. . View in PubMed

ATS Sch. 2020 Jul 24; 1(3):278-287. . View in PubMed

Mental stress causes vasoconstriction in subjects with sickle cell disease and in normal controls Haematologica. 2020 01; 105(1):83-90. . View in PubMed

Progressive vasoconstriction with sequential thermal stimulation indicates vascular dysautonomia in sickle cell disease Blood. 2020 09 03; 136(10):1191-1200. . View in PubMed

Erythrocyte and plasma oxidative stress appears to be compensated in patients with sickle cell disease during a period of relative health, despite the presence of known oxidative agents Free Radic Biol Med. 2019 09; 141:408-415. . View in PubMed

Sickle cell microvascular paradox-oxygen supply-demand mismatch Am J Hematol. 2019 06; 94(6):678-688. . View in PubMed

Early Use of Anti-influenza Medications in Hospitalized Children With Tracheostomy Pediatrics. 2019 03; 143(3). . View in PubMed

Sickle Cell Disease Subjects Have a Distinct Abnormal Autonomic Phenotype Characterized by Peripheral Vasoconstriction With Blunted Cardiac Response to Head-Up Tilt Front Physiol. 2019; 10:381. . View in PubMed

A Retrospective Review of Infants Receiving Sildenafil J Pediatr Pharmacol Ther. 2018 Mar-Apr; 23(2):100-105. . View in PubMed

Upper Airway Narrowing during Central Apnea in Obese Adolescents Ann Am Thorac Soc. 2018 12; 15(12):1465-1471. . View in PubMed

Refining the Application of Microbial Lipids as Tracers of Staphylococcus aureus Growth Rates in Cystic Fibrosis Sputum J Bacteriol. 2018 12 15; 200(24). . View in PubMed

Case Report of Pediatric Channelopathies With UNC80 and KCNJ11 Mutations Having Abnormal Respiratory Control Treated With Positive Airway Pressure Therapy J Clin Sleep Med. 2018 08 15; 14(8):1419-1425. . View in PubMed

A novel cross-correlation methodology for assessing biophysical responses associated with pain J Pain Res. 2018; 11:2207-2219. . View in PubMed

Individuals with sickle cell disease have a significantly greater vasoconstriction response to thermal pain than controls and have significant vasoconstriction in response to anticipation of pain Am J Hematol. 2017 Nov; 92(11):1137-1145. . View in PubMed

Magn Reson Med. 2017 06; 77(6):2364-2371. . View in PubMed

Biophysical markers of the peripheral vasoconstriction response to pain in sickle cell disease PLoS One. 2017; 12(5):e0178353. . View in PubMed

A physician survey reveals differences in management of idiopathic pulmonary hemosiderosis Orphanet J Rare Dis. 2015 Aug 20; 10:98. . View in PubMed

Chronic transfusion therapy improves but does not normalize systemic and pulmonary vasculopathy in sickle cell disease Blood. 2015 Aug 06; 126(6):703-10. . View in PubMed

Autonomic responses to cold face stimulation in sickle cell disease: a time-varying model analysis Physiol Rep. 2015 Jul 14; 3(7). . View in PubMed

Sputum glucose and glycemic control in cystic fibrosis-related diabetes: a cross-sectional study PLoS One. 2015; 10(3):e0119938. . View in PubMed

Pulmonary function abnormalities in childhood cancer survivors treated with bleomycin Pediatr Blood Cancer. 2014 Sep; 61(9):1679-84. . View in PubMed

A diagnosis of exclusion: a 3-year-old boy with respiratory distress and anemia Hosp Pediatr. 2013 Oct; 3(4):377-80. . View in PubMed

Patients with sickle cell anemia on simple chronic transfusion protocol show sex differences for hemodynamic and hematologic responses to transfusion Transfusion. 2013 May; 53(5):1059-68. . View in PubMed

Exercise performance in thalassemia major: correlation with cardiac iron burden Am J Hematol. 2013 Mar; 88(3):193-7. . View in PubMed

Pulmonary function in thalassaemia major and its correlation with body iron stores Br J Haematol. 2011 Oct; 155(1):102-5. . View in PubMed

Peripheral vasoconstriction and abnormal parasympathetic response to sighs and transient hypoxia in sickle cell disease Am J Respir Crit Care Med. 2011 Aug 15; 184(4):474-81. . View in PubMed

Time-varying analysis of autonomic control in response to spontaneous sighs in sickle cell anemia Annu Int Conf IEEE Eng Med Biol Soc. 2010; 2010:1626-9. . View in PubMed

Protein kinase C betaII regulates Akt phosphorylation on Ser-473 in a cell type- and stimulus-specific fashion J Biol Chem. 2004 Nov 12; 279(46):47720-5. . View in PubMed

Tec kinases mediate sustained calcium influx via site-specific tyrosine phosphorylation of the phospholipase Cgamma Src homology 2-Src homology 3 linker J Biol Chem. 2004 Sep 03; 279(36):37651-61. . View in PubMed

Sustained correction of B-cell development and function in a murine model of X-linked agammaglobulinemia (XLA) using retroviral-mediated gene transfer Blood. 2004 Sep 01; 104(5):1281-90. . View in PubMed

A Ras activation pathway dependent on Syk phosphorylation of protein kinase C Proc Natl Acad Sci U S A. 2003 Aug 05; 100(16):9470-5. . View in PubMed

PKC-beta controls I kappa B kinase lipid raft recruitment and activation in response to BCR signaling Nat Immunol. 2002 Aug; 3(8):780-6. . View in PubMed